• Print ISSN: 2395 - 1400, Online ISSN: 2455 - 8923

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Case Report

Epidermolysis Bullosa Acquisita: A rare immune-bullous disorder- A case report

1Professor & Head, 2Assistant professor, 3Post Graduate, Department of Dermatology and Venereology, Kamineni Institute of Medical Sciences, Narketpally, Nalgonda District, Telangana State, India.

ABSTRACT

Epidermolysis bullosa acquisita (EBA) is a chronic mucocutaneous autoimmune blistering disease characterised by skin fragility, blistering at the sites of trauma resulting in scarring and formation of milia. A 21 years old female patient presented with complaints of tense fluid filled lesions on and off since 3 years. There was a history of trauma provoking the onset of lesions and lesions always healed with scarring. There was no family history of similar complaints. She was diagnosed as EBA based on clinical examination, histopathology and immunofloroscence study. Patient was treated with oral prednisolone and dapsone, responded well and was in remission. We are presenting this as an interesting rare case.

Key words :Direct immunofluoroscence, epidermolysis bullosa acquisita, scarring, trauma.